Abstract:

 Objective To investigate the diagnosis and treatment of adult congenital cholangi-ectasis. Methods The clinical data of 33 adult patients from January 2005 to May 2016 were retrospec-tively analyzed. Results The 33 case included type I in 26 cases, type IV in 3 cases, and Type V in 4 cases. Two patients completed the treatment in two phases. The remaining 31 patients underwent one-stage treatment. Conclusion MR + MRCP has a high preoperative diagnosis rate. The specific operation mode should be decided according to the patient′ s specific condition, preoperative examination, Todani type. Surgery congenital choledochocyst should be to remove cystic dilatation of the bile duct as fully as possible according to MRCP or cholangiography as far as possible.

Key words: adult, congenital cholangiectasis, diagnosis and treatment

摘要：

目的 探讨成人先天性胆管扩张症的诊治方法。方法 回顾分析2005年1月至2016年5月我科收治的先天性胆管扩张症33例患者的临床资料。结果 33例患者根据Todani分型：Ⅰ型26例，Ⅳ型3例，Ⅴ型4例。有2例因病情危重分二期手术完成治疗，其余31例均一期手术完成治疗。结论 上腹部MR+MRCP具有高的诊断率，应作为临床检查诊断首选；先天性胆管扩张症的治疗应结合Todani分型，病人的整体情况及病情缓急等决定的治疗方式，术中应结合MRCP或胆道造影尽可能完整切除囊性扩张的胆管。

关键词: 成人, 诊治, 先天性胆管扩张症