Abstract: Objective To investigate the anesthesia management of Sturge-Werber syndrome. Methods The anesthesia management of a child with Sturge-Werber syndrome （type Ⅲ） was retrospectively analyzed， and the related literatures were reviewed. Result After sufficient preoperative evaluation， knowing the patient′s history of antiepilepsy and excluding the risks such as difficult airway and high intraocular pressure， the operation was successfully completed under combined intravenous and inhalation anesthesia， and the patient recovered well after operation. Conclusion Difficult airway， oral and upper respiratory angiomata， central nervous system lesions and glaucoma are the main problems in SWS anesthesia management. Anesthesiologists should fully understand these problems and make appropriate preoperative evaluation of SWS patients so as to formulate appropriate anesthesia management plan.

Key words: anesthesia management, epilepsy, angiomata, Sturge-Werber syndrome, difficult airway

摘要： 目的 探讨Sturge-Werber综合症（SWS）的麻醉管理。方法 回顾分析1例Sturge-Werber综合症（Ⅲ型）患儿的麻醉管理，并对相关文献进行复习。结果 经过充分的术前评估，了解患者的抗癫痫病史并排除困难气道、眼压增高等风险后，患儿在静吸复合麻醉下顺利完成手术，术后恢复良好。结论 困难气道、口腔和上呼吸道血管瘤、中枢神经系统病变、青光眼等是SWS麻醉管理所面临的主要问题。麻醉医师应该充分了解这些问题，并对Sturge-Werber综合症患者进行适当的术前评估从而制定合适的麻醉管理方案。

关键词: Sturge-Werber综合症, 血管瘤, 困难气道, 癫痫, 麻醉管理