Abstract: Objective To investigate the clinical and imaging features of pseudomyogenic hemangioendothelioma. Methods A case of pseudomyogenic hemangioendothelioma in our hospital was analyzed， including clinical features， laboratory test results， image findings and pathological features. Results After laboratory test and imageological examinations， the patient underwent right iliac bone mass and right hip subcutaneous mass resection， he recovered well thereafter. Conclusion Pseudomyogenic hemangioendothelioma is rare， andit manifest as intermediate malignancy or low malignancy. It has the characteristics of soft tissue tumor on imaging and should be differentiated in diagnosis. Familiarity with clinical manifestations， relative imaging features and pathological features is conducive to diagnosis and differential diagnosis of this disease.

Key words: soft tissue tumor, magnetic resonance imaging, computed tomography, pseudomyogenic hemangioendothelioma

摘要： 目的 探讨假肌源性血管内皮瘤的临床及影像学表现。方法 分析我院一例假肌源性血管内皮瘤的临床表现、实验室检查、影像学及病理学特征，并结合文献进行回顾，总结该病的临床、病理及影像学特征。结果 患者进行实验室及影像学检查后，行右侧髂骨肿物及右臀部皮下肿物切除术，术后恢复良好。结论 假肌源性血管内皮瘤是一种少见的低~中度恶性的血管内皮瘤，影像学上具有软组织肿瘤的特点，熟悉其临床表现、影像学及病理学特征，有助于对该病的诊断及鉴别诊断。

关键词: 软组织肿瘤, 计算机断层扫描, 磁共振成像, 假肌源性血管内皮瘤