Research progress on moyamoya disease

doi:10.3969/j.issn.1009-976X.2023.03.013

Abstract

Abstract: Moyamoya disease, also known as spontaneous basilar artery occlusion, is a disease characterized by slow thickening of the intima at the end of the internal carotid artery and the beginning of the anterior cerebral artery and middle cerebral artery, the gradual narrowing and occlusion of the lumen of the artery, and compensatory expansion of Perforate the artery at the base of the brain. This article will review the epidemiological features and clinical features of moyamoya disease in Eastern Asia in recent years.

Key words: Moyamoya disease, spontaneous basilar artery ring occlusion sign, East Asia

摘要： 烟雾病又称自发性基底动脉环闭塞症,是一种以颈内动脉末端及大脑前、大脑中动脉起始部动脉内膜缓慢增厚,动脉管腔逐渐狭窄以至闭塞,脑底穿通动脉代偿性扩张为特征的疾病。本篇文章将对近年来烟雾病的东亚流行病学特征及其临床特点作一综述。

关键词: 烟雾病, 自发性基底动脉环闭塞征, 东亚

CLC Number:

R651.1

WANG Yu-bo, MA Lin, REN He-cheng, LUO Bin, HUANG Ying. Research progress on moyamoya disease[J]. Lingnan Modern Clinics In Surgery, 2023, 23(03): 283-288.

王玉波, 罗斌, 马琳, 任贺成, 尹龙, 黄楹. 烟雾病的研究进展[J]. 岭南现代临床外科, 2023, 23(03): 283-288.

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