Abstract: Objective To analyze the clinical, imaging, pathological features and treatment of hepatic angiomyolipoma （HAML）. Methods Five cases of hepatic angiomyolipoma admitted to our hospital from January 2016 to October 2020 were retrospectively analyzed, and the disease was discussed in combination with relevant literature. Results All the 5 patients with hepatic angiomyolipoma received surgical treatment with good prognosis. During the postoperative follow-up, no tumor recurrence or metastasis was observed in all the patients, and no cases died. Conclusion Hepatic angiomyolipoma is rare in clinical practice, often lack of characteristic clinical manifestations, and early diagnosis is difficult.The diagnosis depends on postoperative pathological and immunohistochemical results. Surgical treatment is the first choice of treatment, which has definite curative effect and good prognosis.

Key words: hepatic angiomyolipoma, liver resection, HMB45

摘要： 目的 探讨肝血管平滑肌脂肪瘤（HAML）的临床、影像学、病理学特点及治疗方法。方法 回顾性分析我院2016年1月至2020年10月间收治的5例肝血管平滑肌脂肪瘤病例,并结合相关文献对本病进行探讨。结果 5例肝血管平滑肌脂肪瘤病人均经外科手术治疗,预后良好,所有病人术后随访期间,未见肿瘤复发及转移,无死亡病例。结论 肝血管平滑肌脂肪瘤临床罕见,常缺乏特征性临床表现,早期诊断困难。明确诊断有赖于术后病理及免疫组化结果。治疗方案首选手术治疗,其疗效确切,预后良好。

关键词: 肝血管平滑肌脂肪瘤, 肝切除, HMB45