Abstract: 【Abstract】 Kasabach-Merritt syndrome (KMS) is a rare clinical disease, which is mainly characterized by large hemangioma with thrombocytopenia. There is no unified standard of treatment and a good radical cure method, and the main method is symptomatic treatment. Most KMS occur in infants and even in neonates. The patients may be accompanied by thrombocytopenia and consumption coagulopathy. For those cases of surgical resection, surgery and anesthesia risk is very high. This paper reports a case of neonatal KMS, discuss anesthesia in children and experience of the authors.

Key words: neonates, Kasabach-Merritt syndrome, Anaesthesia

摘要： 【摘要】〓Kasabach-Merritt综合征(KMS)是一个临床罕见疾病,主要表现为巨大血管瘤合并血小板减少,目前尚没有统一的治疗标准和良好的根治方法,主要行对症治疗。大部分KMS发生在婴幼儿甚至新生儿,患者可能同时伴有血小板减少和消耗性凝血障碍,对于可以手术切除的病例,手术和麻醉的风险很大。本文报道一例新生儿KMS,就患儿的麻醉过程及作者经验进行讨论。