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岭南现代临床外科 ›› 2022, Vol. 22 ›› Issue (03): 306-308.DOI: 10.3969/j.issn.1009-976X.2022.03.018

• 病例报道 • 上一篇    下一篇

一例极低体重儿Caroli综合征行腹腔镜下肝门部囊肿切除术的麻醉管理

刘婷, 许冬妮, 卢桠楠*   

  1. 中山大学孙逸仙纪念医院麻醉科,广州 510120
  • 通讯作者: * 卢桠楠,Email:luynan@mail.sysu.edu.cn
  • 基金资助:
    广东省自然科学基金(2021A1515012357)

Anesthesia management of a very low weight infant with Caroli syndrome undergoing laparoscopic hilar cyst resection

LIU Ting, XU Dong-ni, LU Ya-nan   

  1. Department of Anesthesia, Sun Yat-sen Memorial Hospital, Sun Yat-sen University, Guangzhou 510120, China
  • Received:2021-10-26 Online:2022-06-20 Published:2022-08-09
  • Contact: LU Ya-nan, luynan@mail.sysu.edu.cn

摘要: Caroli综合征又称先天性肝内胆管囊性扩张症并伴有先天性肝纤维化,是一种罕见的小儿先天性疾病。对于弥漫性病变累及的患者,选择的治疗方法是原位肝移植。本例为6月龄女婴,发育严重落后,体重仅为3.8kg,腹胀明显,合并大量腹水、贫血,为延长等待肝移植的时间,拟行腹腔镜下胆总管囊肿切除后肝总管空肠吻合术,使麻醉管理具有挑战性,现将我院诊治的一例Caroli综合征的麻醉汇报并做文献复习,并探讨低体重患儿的麻醉管理。

关键词: Caroli综合征, 低体重患儿, 麻醉管理

Abstract: Caroli syndrome, also known as congenital cystic dilatation of intrahepatic bile duct accompanied by congenital liver fibrosis, is a rare congenital disease in children. For patients with diffuse disease involvement, orthotopic liver transplantation is the choice of treatment. This casewas a 6-month-old female infant, development lagging behind, weighsonly 3.8 kg, had abdominal distension, with massive ascites and anemia, In order to prolong the waiting time for liver transplantation, she plans to undergo laparoscopic choledochal cyst resection and hepatic duct jejunostomy. Anesthesia management is challenging. Now we will report an anesthesia case of Caroli syndrome diagnosed and treated in our hospital and do a literature review, and discuss the anesthesia management of low birth weight children.

Key words: caroli syndrome, low birth weight children, anesthesia management

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