关键词: Caroli综合征, 低体重患儿, 麻醉管理

Abstract: Caroli syndrome, also known as congenital cystic dilatation of intrahepatic bile duct accompanied by congenital liver fibrosis, is a rare congenital disease in children. For patients with diffuse disease involvement, orthotopic liver transplantation is the choice of treatment. This casewas a 6-month-old female infant, development lagging behind, weighsonly 3.8 kg, had abdominal distension, with massive ascites and anemia, In order to prolong the waiting time for liver transplantation, she plans to undergo laparoscopic choledochal cyst resection and hepatic duct jejunostomy. Anesthesia management is challenging. Now we will report an anesthesia case of Caroli syndrome diagnosed and treated in our hospital and do a literature review, and discuss the anesthesia management of low birth weight children.

Key words: caroli syndrome, low birth weight children, anesthesia management