关键词: 肝血管平滑肌脂肪瘤, 误诊, 肝癌

Abstract: 【Abstract】〓Objective〓To investigate clinical characteristic, pathological and immunohistochme-ical features, diagnosis and treatment of hepatic angiomyolipoma (HAML). Methods〓One case misdiagn-osed as hepatic carcinoma was retrospectively analyzed and confirmed by pathological examination for huge hepatic angiomyolipoma in our hospital. The clinical presentation, imaging performance, pathological and immunohistochmeical features combining with the knowledge were reviewed. Results〓Most patients with HAML were asymptomatic, and occur commonly in female. HAML are composed of varying amounts of smooth muscle cells, adipose tissue, and vessels. Immunohistochemeical staining showed the tumor cells were positive for HMB45, Melan-A and SMA. Conclusion〓HAML lacks typical clinical presentation, its imaging appearance varies widely, easily misdiagnosed as other tumors. Liver biopsy is proposed when it is difficult to get a clear diagnosis. The reliable way to diagnose HAML is depend on pathology and immunohistochemical technique.

Key words: Hepatic angiomyolipoma, Misdiagnose, Hepatic carcinoma